(C4) Butyrylcarnitine
目录号 | 数量 | 价格 | 提前通知时间 | 购买此产品 |
---|---|---|---|---|
4266-1mg | 1 mg | 请查询 | 7 天 |
Butyrylcarnitine, also known as (3R)-3-(butyryloxy)-4-(trimethylammonio)butanoate or L-carnitine butyryl ester, is classified as a member of the acylcarnitines. Acylcarnitines are organic compounds containing a fatty acid with the carboxylic acid attached to carnitine through an ester bond. Butyrylcarnitine may be used as an analytical reference standard for the separation and identification of underivatized butyryl-L-carnitine in human plasma samples using high-performance liquid chromatography coupled to tandem mass spectrometry (HPLC-MS/MS).
Butyrylcarnitine can be used to study its role in energy production and its metabolic effects, to understand metabolic diseases and conditions associated with mitochondrial dysfunction. Butyrylcarnitine is a major biological marker of short-chain acyl-CoA dehydrogenase deficiency, glutaric acidemia type II and isobutyrylglycinuria, and ethylmalonic encephalopathy.
The product is used primarily as a control for MS/MS.
General properties
Appearance: | white solid |
Molecular weight: | 267.75 |
CAS number: | 162067-50-7 (chloride), 25576-40-3 (inner salt) |
Molecular formula: | C11H22ClNO4 |
Solubility: | DMSO, DMF, ethanol |
Quality control: | NMR 1H and HPLC-MS (95+%) |
Storage conditions: | 24 months after receival at -20°C in the dark. Transportation: at room temperature for up to 3 weeks. Desiccate. |
安全数据表(MSDS): | 下载 |
产品规格 |
